Lung structure-function correlation in patients with primary ciliary dyskinesia
نویسندگان
چکیده
منابع مشابه
Lung structure and function similarities between primary ciliary dyskinesia and mild cystic fibrosis: a pilot study
BACKGROUND Primary ciliary dyskinesia (PCD) and cystic fibrosis (CF) are increasingly compared. There are no chest magnetic resonance imaging (MRI) comparative studies of PCD and CF. We assessed clinical, functional, microbiological and MRI findings in PCD and mild CF patients in order to evaluate different expression of lung disease. METHODS Twenty PCD (15.1 years) and 20 CF subjects with mi...
متن کاملPrimary ciliary dyskinesia.
Primary ciliary dyskinesia (PCD) is a rare genetic condition that affects the ciliary function of the respiratory tract, sperm tail, cilia of the embryonic node, and fallopian tube. The condition is characterized by impaired ciliary action, leading to recurrent lower-respiratory-tract infections, bronchiectasis, rhino-sinusitis, otitis media, impaired fertility in women, and infertility in men....
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Primary ciliary dyskinesia is a rare, autosomal recessive disease, with diminished ciliary motility resulting in chronic disease of the upper and lower airway. Due to its low prevalence, there are few studies with significant numbers of cases, and a lack of guidelines for the management of this group of patients. Most patients present chronic rhinosinusitis at diagnosis and while there is impro...
متن کاملImpaired Growth during Childhood in Patients with Primary Ciliary Dyskinesia
Primary ciliary dyskinesia (PCD) leads to recurrent/chronic respiratory infections, resulting in chronic inflammation and potentially in chronic pulmonary disease with bronchiectasis. We analyzed longitudinal data on body length/height and body mass index (BMI) for 29 children and young adults with PCD aging 1.5-24 years (median, 14.5) who had been diagnosed at the age of 0.5-17 years (median, ...
متن کاملPrimary ciliary dyskinesia: the patients grow up.
Affiliations: Institute of Social and Preventive Medicine, University of Bern, Bern, Switzerland. Paediatric Respiratory Medicine, Children’s University Hospital of Bern, University of Bern, Bern, Switzerland. Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK. NIHR Southampton Respiratory Biomedical Research Unit, University of Southampton ...
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ژورنال
عنوان ژورنال: Thorax
سال: 2015
ISSN: 0040-6376
DOI: 10.1136/thoraxjnl-2014-206578